Neutropenia-monocytopenia-deafness syndrome

Orpha code: 2690OMIM code:

Definition

Neutropenia-monocytopenia-deafness syndrome is characterised by neutropenia with myeloid marrow hypoplasia, monocytopenia, and congenital deafness. It has been described in three siblings who suffered recurrent bacterial infections.

Disease data
Classification

Disease

Synonyms
Neutropenia-monocytopenia-hearing loss syndrome
ORPHA code
2690
OMIM code
-
ICD10 code
D82.8
ICD11 code
-

No additional description.

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