Isolated posterior meningocele

Orpha code: 268810OMIM code:

Definition

Posterior meningocele is a rare neural tube closure defect characterized by the herniation of a cerebrospinal fluid-filled sac, that is lined by dura and arachnoid mater, through a posterior spina bifida and covered by a layer of skin of variable thickness, which may be dysplastic or ulcerated. The spinal cord and nerves are generally not included and function normally, although sometimes a tethered cord may be associated. They are most commonly located in the lumbar or sacral region.

Disease data
Classification

Morphological anomaly

ORPHA code
268810
OMIM code
-
ICD10 code
Q05.2
ICD11 code
LA02.0Y

No additional description.

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