Intraocular medulloepithelioma

Orpha code: 268139OMIM code:

Definition

Intraocular medulloepithelioma is a rare eye tumor characterized by a white, gray or yellow-colored cystic mass that arises from the primitive neuroectodermal, nonpigmented epithelium of the ciliary body, or occasionally from the optic nerve, optic disc, retina or iris. Typically it has a benign clinical course with good prognosis and generally presents with childhood onset of poor vision and pain, glaucoma, and/or cataract. Leukocoria, exotropia, exophthalmos, strabismus, epiphora, change in eye color, hyphema, and raised intraocular pressure are also remarkable manifestations.

Disease data
Classification

Disease

Synonyms
Orbital medulloepithelioma
Nabłoniak rdzeniakowy oczodołu
ORPHA code
268139
OMIM code
-
ICD10 code
D31.4
ICD11 code
-

No additional description.

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