Isolated pulmonary capillaritis

Definition

Isolated pauciimmune pulmonary capillaritis is a small vessel vasculitis restricted to the lungs that may induce diffuse alveolar hemorrhage with dyspnea, anemia, chest pain, hemoptysis, bilateral and diffuse alveolar infiltrates at chest X-rays, without any underlying systemic disease. ANCA are frequently positive but could be negative.

Disease data

Classification

Disease

ORPHA code

264691

OMIM code

ICD10 code

J84.8

ICD11 code

CB04.4

*Soruce