Generalized peeling skin syndrome

Orpha code: 263543OMIM code: 270300

Definition

A form of peeling skin syndrome characterized by a generalized distribution. It comprises two sub-types: the non-inflammatory (PSS type A) and the inflammatory (PSS type B) form. PSS type A is characterized by generalized white scaling with superficial non-inflammatory peeling of the skin, while PSS type B is characterized by superficial patchy peeling of the entire skin with underlying erythroderma, pruritus, and atopy.

Disease data
Classification

Disease

Synonyms
Generalized PSS
Generalized deciduous skin
ORPHA code
263543
OMIM code
270300
ICD10 code
Q80.8
ICD11 code
EC20.1

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl