CHST3-related skeletal dysplasia

Orpha code: 263463OMIM code: 143095

Definition

CHST3-related skeletal dysplasia is a very rare bone disorder characterized clinically by short stature of prenatal onset; dislocation of the knees, hips or elbows; club feet; limitation of range of motion of large joints; progressive kyphosis; and occasional scoliosis. In a few patients, minor heart valve dysplasia has also been described. Intellect, vision and hearing are normal.

Disease data
Classification

Disease

Synonyms
Chondrodysplasia with congenital joint dislocations, CHST3 type
Chondrodysplazja z wrodzonym zwichnięciem stawów, typu CHST3
Dysplazja kręgosłupowo-nasadowa z wrodzonym zwichnięciem stawów, typu CHST3
SDCD, CHST3 type
Spondyloepiphyseal dysplasia with congenital joint dyslocations, CHST3 type
ORPHA code
263463
OMIM code
143095
ICD10 code
Q74.8
ICD11 code
LD24.3

No additional description.

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