Nevus of Ito

Orpha code: 263432OMIM code:

Definition

Nevus of Ito is a benign dermal melanocytosis occurring most frequently in the Asian populations and characterized by unilateral, asymptomatic, blue, gray or brown skin pigmentation within the acromioclavicular and upper chest area (involving the side of the neck, the supraclavicular and scapular areas, and the shoulder region). It is usually diagnosed in early infancy and in early adolescence. Nevus of Ito may progressively enlarge and darken in color (particularly with puberty) and its appearance usually remains stable once adulthood is reached. Spontaneous regression does not occur. Malignant melanoma has rarely been reported within a nevus of Ito. It shares the clinical features of nevus of Ota, except its anatomic location and in rare occasions, mayoccur together with the latter.

Disease data
Classification

Disease

Synonyms
Nevus fuscocaeruleus acromiodeltoideus
ORPHA code
263432
OMIM code
-
ICD10 code
D22.6
ICD11 code
LC10

No additional description.

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