Mitochondrial myopathy and sideroblastic anemia

Orpha code: 2598OMIM code: 613561

Definition

Mitochondrial myopathy and sideroblastic anemia belongs to the heterogeneous family of metabolic myopathies. It is characterised by progressive exercise intolerance manifesting in childhood, onset of sideroblastic anaemia around adolescence, lactic acidaemia, and mitochondrial myopathy.

Disease data
Classification

Disease

Synonyms
MLASA
Miopatia, kwasica mleczanowa i niedokrwistość syderoblastyczna
MLASA
MSA
Myopathy, lactic acidosis and sideroblastic anemia
ORPHA code
2598
OMIM code
613561
ICD10 code
G71.3
ICD11 code
3A72.0Y

No additional description.

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