Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare benign peripheral nerve sheath tumor characterized by a usually encapsulated space-occupying lesion composed of differentiated neoplastic Schwann cells. It most commonly arises from peripheral nerves in the head and neck region and extensor aspects of the extremities, but also from spinal and cranial nerves, especially the vestibular nerve. The tumor may be asymptomatic or cause symptoms related to a mass effect. It grows slowly and only rarely undergoes malignant transformation. Disease data Classification Disease Synonyms Neurilemmoma Fibroblastoma obwodowa Neurilemmoma Neurilemoma Neurolemmoma Neurilemoma Peripheral fibroblastoma ORPHA code 252164 OMIM code - ICD10 code D36.1 ICD11 code 2F3Y *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl