Benign schwannoma

Orpha code: 252164OMIM code:

Definition

A rare benign peripheral nerve sheath tumor characterized by a usually encapsulated space-occupying lesion composed of differentiated neoplastic Schwann cells. It most commonly arises from peripheral nerves in the head and neck region and extensor aspects of the extremities, but also from spinal and cranial nerves, especially the vestibular nerve. The tumor may be asymptomatic or cause symptoms related to a mass effect. It grows slowly and only rarely undergoes malignant transformation.

Disease data
Classification

Disease

Synonyms
Neurilemmoma
Fibroblastoma obwodowa
Neurilemmoma
Neurilemoma
Neurolemmoma
Neurilemoma
Peripheral fibroblastoma
ORPHA code
252164
OMIM code
-
ICD10 code
D36.1
ICD11 code
2F3Y

No additional description.

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