Extraventricular neurocytoma

Orpha code: 251927OMIM code:

Definition

Extraventricular neurocytoma (EVN), a variant of central neurocytoma (see this term), is a rare neuronal neoplasm, composed of round cells with neuronal differentiation, which is located outside of the ventricular system, usually within the spinal cord or cerebral hemispheres and that manifests with headache, nausea, vomiting, complex partial seizures or focal neurological deficits. In some cases it may exhibit atypical features consistent with aggressive clinical behavior.

Disease data
Classification

Disease

Synonyms
EVN
ORPHA code
251927
OMIM code
-
ICD10 code
C72.9
ICD11 code
-

No additional description.

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