Pineoblastoma

Definition

Pineoblastoma is a rare, malignant type of supratentorial primitive neuroectodermal tumor (sPNET), found mainly in children (less than 10% of cases are reported in adults), and located in the pineal region of the brain but that can metastasize along the neuroaxis. As it is the most aggressive of the pineal parenchymal tumors, it is usually associated with a poor prognosis.

Disease data

Classification

Disease

ORPHA code

251909

OMIM code

ICD10 code

C75.3

ICD11 code

2A00.20

*Soruce