Ependymoblastoma

Definition

Ependymoblastoma is a rare type of primitive neuroectodermal tumor (PNET) that usually occurs in young children under the age of 2 and is histologically distinguished by the production of ependymoblastic rosettes. It is associated with an aggressive course and a poor prognosis.

Disease data

Classification

Disease

ORPHA code

251880

OMIM code

ICD10 code

C71.9

ICD11 code

2A00.11

*Soruce