Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Medulloblastoma with extensive nodularity (MBEN) is a histological variant of medulloblastoma (see this term), an embryonic malignancy, most often located in the inferior medullary velum and then growing into the fourth ventricle, and presenting in infants and young children with symptoms of increased intracranial pressure such as headache, listlessness, vomiting, diplopia and papilledema. It is often associated with Gorlin syndrome (see this term) and has a relatively good prognosis. Disease data Classification Histopathological subtype Synonyms MBEN Nerwiak zarodkowy móżdżku ORPHA code 251858 OMIM code 155255 ICD10 code C71.6 ICD11 code 2A00.10 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl