Description of the disease * EnglishPolish Pobierz sekcję do PDF Definicja Medulloblastoma with extensive nodularity (MBEN) is a histological variant of medulloblastoma (see this term), an embryonic malignancy, most often located in the inferior medullary velum and then growing into the fourth ventricle, and presenting in infants and young children with symptoms of increased intracranial pressure such as headache, listlessness, vomiting, diplopia and papilledema. It is often associated with Gorlin syndrome (see this term) and has a relatively good prognosis. Disease data Klasyfikacja Histopathological subtype Synonimy MBEN Nerwiak zarodkowy móżdżku Kod ORPHA 251858 Kod OMIM 155255 Kod ICD10 C71.6 Kod ICD11 2A00.10 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl