Medulloblastoma with extensive nodularity

Orpha code: 251858OMIM code: 155255

Definition

Medulloblastoma with extensive nodularity (MBEN) is a histological variant of medulloblastoma (see this term), an embryonic malignancy, most often located in the inferior medullary velum and then growing into the fourth ventricle, and presenting in infants and young children with symptoms of increased intracranial pressure such as headache, listlessness, vomiting, diplopia and papilledema. It is often associated with Gorlin syndrome (see this term) and has a relatively good prognosis.

Disease data
Classification

Histopathological subtype

Synonyms
MBEN
Nerwiak zarodkowy móżdżku
ORPHA code
251858
OMIM code
155255
ICD10 code
C71.6
ICD11 code
2A00.10

No additional description.

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