Medulloblastoma with extensive nodularity

Orpha code: 251858OMIM code: 155255

Definicja

Medulloblastoma with extensive nodularity (MBEN) is a histological variant of medulloblastoma (see this term), an embryonic malignancy, most often located in the inferior medullary velum and then growing into the fourth ventricle, and presenting in infants and young children with symptoms of increased intracranial pressure such as headache, listlessness, vomiting, diplopia and papilledema. It is often associated with Gorlin syndrome (see this term) and has a relatively good prognosis.

Disease data
Klasyfikacja

Histopathological subtype

Synonimy
MBEN
Nerwiak zarodkowy móżdżku
Kod ORPHA
251858
Kod OMIM
155255
Kod ICD10
C71.6
Kod ICD11
2A00.10

No additional description.

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