Idiopathic recurrent pericarditis

Orpha code: 251307OMIM code:

Definition

Idiopathic recurrent pericarditis is a rare autoinflammatory syndrome defined as recurrence of pericardial inflammation of unknown origin following the first episode of acute pericarditis and a symptom-free interval of 4-6 weeks or longer. Recurrent attacks of chest pain may be the sole presentation or the chest pain may be accompanied by pericardial friction rub, electrocardiographic or echocardiographic changes, pericardial effusion and increased C-reactive protein. Cardiac tamponade is a rare, life-threatening complication.

Disease data
Classification

Disease

Synonyms
Idiopathic relapsing pericarditis
ORPHA code
251307
OMIM code
-
ICD10 code
I09.2
ICD11 code
-

No additional description.

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