Pigmented paravenous retinochoroidal atrophy

Orpha code: 251295OMIM code: 172870

Definition

Pigmented paravenous retinochoroidal atrophy (PPRCA) is a rare, commonly bilateral and symmetric retinal disease characterized by non-progressive or slowly progressive chorioretinal atrophy, peripapillary pigmentary changes and accumulation of ''bone-corpuscle'' pigmentation along the retinal veins and which is usually asymptomatic or can present with mild blurred vision.

Disease data
Classification

Disease

Synonyms
PPRCA
PPRCA
ORPHA code
251295
OMIM code
172870
ICD10 code
H35.5
ICD11 code
9B7Y

No additional description.

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