Pigmented paravenous retinochoroidal atrophy

Orpha code: 251295OMIM code: 172870

Definicja

Pigmented paravenous retinochoroidal atrophy (PPRCA) is a rare, commonly bilateral and symmetric retinal disease characterized by non-progressive or slowly progressive chorioretinal atrophy, peripapillary pigmentary changes and accumulation of ''bone-corpuscle'' pigmentation along the retinal veins and which is usually asymptomatic or can present with mild blurred vision.

Disease data
Klasyfikacja

Disease

Synonimy
PPRCA
PPRCA
Kod ORPHA
251295
Kod OMIM
172870
Kod ICD10
H35.5
Kod ICD11
9B7Y

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl