Autosomal recessive Stickler syndrome

Orpha code: 250984OMIM code: 614284

Definicja

A rare type of Stickler syndrome characterized by moderate to severe sensorineural hearing loss, high myopia, retinal degeneration, vitreous anomalies, and epiphyseal dysplasia. Midface hypoplasia, cleft palate, as well as additional skeletal manifestations (such as platyspondyly, scoliosis, and tibial and femoral bowing at birth) have also been observed.

Disease data
Klasyfikacja

Clinical subtype

Kod ORPHA
250984
Kod OMIM
614284
Kod ICD10
Q87.5
Kod ICD11
LD2F.1Y

No additional description.

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