Inflammatory myopathy with abundant macrophages

Orpha code: 247718OMIM code:

Definicja

A rare idiopathic inflammatory myopathy characterized by diffuse destructive infiltration of CD68+ macrophages into the fascia rather than muscle fibers in muscle biopsies, proximal muscle weakness and myalgia with or without scaly dermatomyositis-like or atypical non-dermatomyositis-like skin lesions, elevation of creatine kinase levels and thickening of muscle fascia in muscle MRI.

Disease data
Klasyfikacja

Disease

Synonimy
IMAM
IMAM
Kod ORPHA
247718
Kod OMIM
-
Kod ICD10
G72.4
Kod ICD11
-

No additional description.

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