Arrhythmogenic right ventricular cardiomyopathy

Orpha code: 247OMIM code:

Definition

A heart muscle disease that consists in progressive dystrophy of primarily the right ventricular myocardium with fibro-fatty replacement and ventricular dilation, and that is clinically characterized by ventricular arrhythmias and a risk of sudden cardiac death.

Disease data
Classification

Clinical group

Synonyms
ARVC
ARVC
ARVD
Arytmogenna dysplazja prawej komory
ARVD
Arrhythmogenic right ventricular dysplasia
ORPHA code
247
OMIM code
-
ICD10 code
I42.8
ICD11 code
BC43.6

No additional description.

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