Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare respiratory malformation characterized by a hamartomatous mass of non-functioning lung tissue of variable extent and with variable degrees of cystic or adenomatoid change. Clinical presentation, prognosis, and presence of associated abnormalities depend on the subtype of the lesion. Based on histopathological findings, five subtypes (types 0 to 4) can be differentiated. Disease data Classification Malformation syndrome Synonyms CCAM CCAM CPAM Congenital cystic adenomatoid malformation of the lung Congenital cystic adenomatous malformation of the lung Congenital cystic disease of the lung ORPHA code 2444 OMIM code - ICD10 code Q33.0 ICD11 code LA75.4 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl