Isolated congenital hypogonadotropic hypogonadism

Orpha code: 238666OMIM code:

Definition

A rare, genetic pituitary hormone deficiency characterized by gonadotropin (Gn) deficiency with low sex steroid levels associated with low levels of follicle stimulating hormone (FSH) and luteinizing hormone (LH). This disorder may be associated with a normal (normosmic) or impaired sense of smell (Kallmann syndrome).

Disease data
Classification

Disease

Synonyms
Gonadotropic deficiency
Isolated congenital gonadotropin deficiency
Isolated gonadotropin-releasing hormone deficiency
Gonadotropic deficiency
Isolated congenital gonadotropin deficiency
Isolated gonadotropin-releasing hormone deficiency
ORPHA code
238666
OMIM code
-
ICD10 code
E23.0
ICD11 code
-

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl