IgG4-related mesenteritis

Orpha code: 238593OMIM code:

Definition

Sclerosing mesenteritis (SM) is a rare pathological disease causing inflammation of the adipose tissue of the small bowel mesentery and is commonly associated with abdominal pain, diarrhea, nausea, weight loss, bloating and loss of appetite. The two subforms include mesenteric panniculitis (where inflammation and fatty necrosis are dominant features) and retractile mesenteritis (where fibrosis and retraction dominate).

Disease data
Classification

Clinical subtype

Synonyms
Isolated mesenteric lipodystrophy
Izolowana lipodystrofia krezki jelitowej
Lipomatous mesenteritis
Tłuszczowo-stwardniające zapalenie krezki jelitowej
Zapalenie tkanki tłuszczowej krezki jelitowej
Ziarniniak tłuszczowy krezki jelitowej
Lipomatous mesenteritis
Liposclerotic mesenteritis
Mesenteric lipogranuloma
Mesenteric panniculitis
Sclerosing mesenteritis
ORPHA code
238593
OMIM code
-
ICD10 code
K65.8
ICD11 code
-

No additional description.

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