Ectopic aldosterone-producing tumor

Orpha code: 231632OMIM code:

Definition

Ectopic aldosterone-producing tumor is an extremely rare aldosterone-producing neoplasm composed of aberrant adrenocortical tissue located outside the adrenal glands (e.g. in retroperitoneum, perirenal or periaortic fatty tissue, thorax, spinal canal, testes, ovaries) typically characterized by symptoms related to increased aldosterone levels (such as sustained, treatment-resistant hypertension and hypokalemia) or symptoms caused by local tumor enlargement.

Disease data
Classification

Disease

Synonyms
Extra-adrenal aldosterone-producing tumor
Extra-adrenal aldosterone-producing tumor
ORPHA code
231632
OMIM code
-
ICD10 code
E26.8
ICD11 code
-

No additional description.

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