Congenital erosive and vesicular dermatosis

Orpha code: 231573OMIM code:

Definition

Congenital erosive and vesicular dermatosis is a rare, idiopathic skin disease characterized by widespread, congenital, superficial erosions and vesicles (often involving more than 75% of the body) which heal leaving scars with a supple, symmetrical, reticulated pattern, frequently resulting in cicatricial alopecia and hyperthermia and/or hypohydrosis. Nail anomalies, neurodevelopmental and ophtalmologic abnormalities, tongue atrophy and preterm birth, with or without history of choriomnionitis, are commonly associated.

Disease data
Classification

Disease

Synonyms
CEVD
Congenital erosive and vesicular dermatosis with reticulated supple scarring
CEVD
Congenital erosive and vesicular dermatosis with reticulated supple scarring
ORPHA code
231573
OMIM code
-
ICD10 code
-
ICD11 code
KC31

No additional description.

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