Mid-dermal elastolysis

Orpha code: 228299OMIM code:

Definicja

A rare, acquired, dermis elastic tissue disease characterized by asymptomatic, well-demarcated, symmetric patches and/or plaques of finely wrinkled skin arranged parallel to skin cleavage lines (type I), associated with perifollicular papular protrusions (type II) or with persistent reticular erythema (type III), occurring predominantly on the shoulders, trunk, back, and proximal extremities, associating, on histopathology, a selective loss of elastic tissue in the midreticular dermis. Erythema and/or urticaria may or may not precede wrinkly lesions.

Disease data
Klasyfikacja

Disease

Kod ORPHA
228299
Kod OMIM
-
Kod ICD10
L98.8
Kod ICD11
EE41.Y

No additional description.

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