Mid-dermal elastolysis

Orpha code: 228299OMIM code:

Definition

A rare, acquired, dermis elastic tissue disease characterized by asymptomatic, well-demarcated, symmetric patches and/or plaques of finely wrinkled skin arranged parallel to skin cleavage lines (type I), associated with perifollicular papular protrusions (type II) or with persistent reticular erythema (type III), occurring predominantly on the shoulders, trunk, back, and proximal extremities, associating, on histopathology, a selective loss of elastic tissue in the midreticular dermis. Erythema and/or urticaria may or may not precede wrinkly lesions.

Disease data
Classification

Disease

ORPHA code
228299
OMIM code
-
ICD10 code
L98.8
ICD11 code
EE41.Y

No additional description.

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