Late-onset focal dermal elastosis

Orpha code: 228227OMIM code:

Definition

Late-onset focal dermal elastosis is a rare, acquired, dermis elastic tissue disorder characterized by a pseudoxanthoma elasticum-like papular eruption consisting of multiple, slowly progressive, asymptomatic, 2-5 mm, white to yellowish, non-follicular papules (that tend to form cobblestone plaques) predominantly distributed over the neck, axillae and flexural areas, with no systemic involvement. Skin biopsy reveals a focal increase of normal-appearing elastic tissue in the reticular dermis with no calcium deposits.

Disease data
Classification

Disease

Synonyms
PXE-like late-onset focal dermal elastosis
Pseudoxanthoma-like late-onset focal dermal elastosis
ORPHA code
228227
OMIM code
-
ICD10 code
L98.8
ICD11 code
-

No additional description.

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