Baló concentric sclerosis

Orpha code: 228165OMIM code:

Definition

A rare multiple sclerosis variant characterized by discrete concentrically layered, ring-like lesions in the cerebral white matter, consisting of alternating layers of myelinated and demyelinated tissue. Patients most commonly present with symptoms of an intracerebral mass lesion, including headache, cognitive abnormalities, behavioral changes, seizures, aphasia, or hemiparesis, among others, although there may also be classic focal symptoms of multiple sclerosis, such as focal weakness, ataxia, sensory disturbance, or diplopia.

Disease data
Classification

Disease

Synonyms
Concentric demyelination
Demielinizacja koncentryczna
ORPHA code
228165
OMIM code
-
ICD10 code
G37.5
ICD11 code
8A40.Y

No additional description.

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