Hughes-Stovin syndrome

Definition

Hughes-Stovin syndrome (HSS) is a life-threatening disorder, believed to be a cardiovascular clinical variant manifestation of Behçet's disease (BD; see this term). It is characterized by the association of multiple pulmonary artery aneurysms (PAAs) and peripheral venous thrombosis.

Disease data

Classification

Disease

ORPHA code

228116

OMIM code

ICD10 code

I28.8

ICD11 code

4A44.Y

*Soruce