Hypoplastic left heart syndrome

Orpha code: 2248OMIM code: 614435

Definition

A rare, congenital, non-syndromic, heart malformation characterized by under development of the left-sided cardiac structures (including left ventricle, ascending aorta, aortic arch, and mitral and/or aortic valve) such that the left heart is unable to provide adequate systemic cardiac output.

Disease data
Classification

Morphological anomaly

Synonyms
HLHS
ORPHA code
2248
OMIM code
614435
ICD10 code
Q23.4
ICD11 code
LA89.3

No additional description.

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