Confetti-like macular atrophy

Orpha code: 221142OMIM code:

Definition

A rare, acquired, dermis elastic tissue disorder with decreased elastic tissue characterized by multiple, asymptomatic, well demarcated, flat, hypopigmented atrophic macular skin lesions distributed over upper trunk and proximal upper limbs. Histopathological examination reveals atrophic epidermis with decreased basal pigmentation, perivascular mononuclear infiltration in the upper dermis, and disorganized, hyalinized, coarse collagen bundles, and variable loss of elastic fibers in the dermis.

Disease data
Classification

Disease

ORPHA code
221142
OMIM code
-
ICD10 code
L90.8
ICD11 code
-

No additional description.

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