Marchiafava-Bignami disease

Orpha code: 221074OMIM code:

Definicja

A rare neurologic disease most prominently characterized by progressive demyelination and necrosis of the corpus callosum. It is in most cases associated with chronic alcoholism and malnutrition. Speed of onset and clinical presentation are very variable with a range of possible symptoms, including dementia, seizures, gait abnormalities, dysarthria, aphasia, athetosis, as well as stupor and coma.

Disease data
Klasyfikacja

Disease

Synonimy
MBD
Kod ORPHA
221074
Kod OMIM
-
Kod ICD10
G37.1
Kod ICD11
8A46

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl