Attenuated familial adenomatous polyposis

Orpha code: 220460OMIM code: 616415

Definition

A mild form of familial adenomatous polyposis characterized by the presence of fewer than 100 adenomatous colonic polyps, a more proximal colonic location, a delayed age of colorectal cancer onset and a more limited expression of the extracolonic features.

Disease data
Classification

Disease

Synonyms
AFAP
AFAP
Poronna FAP
Postać poronna rodzinnej polipowatości jelita grubego
Attenuated FAP
Attenuated familial polyposis coli
ORPHA code
220460
OMIM code
616415
ICD10 code
D12.6
ICD11 code
2B90.Y

No additional description.

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