Limited cutaneous systemic sclerosis

Orpha code: 220402OMIM code: 181750

Definicja

Limited cutaneous systemic sclerosis (lcSSc) is a subtype of systemic sclerosis (SSc; see this term) characterized by the association of Raynaud's phenomenon with skin fibrosis limited to the hands, face, feet and forearms.

Disease data
Klasyfikacja

Clinical subtype

Synonimy
Limited cutaneous systemic scleroderma
Kod ORPHA
220402
Kod OMIM
181750
Kod ICD10
M34.1
Kod ICD11
-

No additional description.

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