Rhabdomyosarcoma of the cervix uteri

Orpha code: 213802OMIM code:

Definition

Rhabdomyosarcoma of the cervix uteri is a rare, highly malignant soft tissue sarcoma located in the uterine cervix and arising from primitive mesenchymal cells displaying skeletal muscle differentiation. It most often presents with abnormal vaginal discharge or dysfunctional uterine bleeding, abdominal pain and/or a cervical mass protruding into the vagina. Association with DICER1 syndrome has been reported.

Disease data
Classification

Disease

Synonyms
Cervical rhabdomyosarcoma
Mięsak prążkowanokomórkowy szyjki
ORPHA code
213802
OMIM code
-
ICD10 code
C53.1
ICD11 code
2B55.Y

No additional description.

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