Primitive neuroectodermal tumor of the corpus uteri

Orpha code: 213630OMIM code:

Definicja

Primitive neuroectodermal tumor of the corpus uteri is a rare cancer of corpus uteri derived from neural crest cells, characterized by small, round neoplastic cells with variable degree of neural, glial and ependymal differentiation. Macroscopically, the tumor is often a large, poorly circumscribed polypoid mass with necrotic areas and hemorrhage. It usually presents with lower abdominal or pelvic pain, irregular vaginal bleeding or discharge, pelvic mass and uterine enlargement.

Disease data
Klasyfikacja

Disease

Synonimy
Malignant peripheral neuroectodermal tumor of the corpus uteri
Obwodowy guz neuroektodermalny trzonu macicy
Złośliwy obwodowy guz neuroektodermalny trzonu macicy
Peripheral neuroectodermal cancer of the corpus uteri
Kod ORPHA
213630
Kod OMIM
-
Kod ICD10
C54.8
Kod ICD11
-

No additional description.

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