Kaposiform hemangioendothelioma

Orpha code: 2122OMIM code:

Definition

A rare low-grade malignant cutaneous or visceral vascular tumour that may be associated with severe thrombopaenia with consumption coagulopathy (Kasabach-Merritt syndrome) in pediatric patients.

Disease data
Classification

Disease

ORPHA code
2122
OMIM code
-
ICD10 code
C49.9
ICD11 code
2F72.Y

No additional description.

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