Autosomal dominant proximal spinal muscular atrophy

Orpha code: 211037OMIM code:

Definicja

A group of rare, genetic, motor neuron disease characterized by childhood or adult onset progressive, predominantly proximal, muscular weakness and wasting. Included diseases are Autosomal dominant adult-onset proximal spinal muscular atrophy, Lower motor neuron syndrome with late-adult onset, and Autosomal dominant childhood-onset proximal spinal muscular atrophy.

Disease data
Klasyfikacja

Clinical group

Kod ORPHA
211037
Kod OMIM
-
Kod ICD10
G12.1
Kod ICD11
-

No additional description.

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