Optic pathway glioma

Orpha code: 2086OMIM code:

Definition

Optic pathway glioma (OPG) is a benign tumor that develop along the optic nerve (chiasm, tracts, and radiations) characterized by impairment or loss of vision and may be accompanied by diencephalic symptoms such as reduced growth and alteration in sleeping patterns. OPG are often linked to neurofibromatosis type 1 (NF1, see this term).

Disease data
Classification

Disease

ORPHA code
2086
OMIM code
-
ICD10 code
D33.3
ICD11 code
2A02.0Y

No additional description.

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