Congenital aortopulmonary window

Orpha code: 2037OMIM code:

Definicja

A rare congenital non-syndromic heart malformation characterized by a communication between the ascending aorta and the pulmonary trunk in the presence of two normally formed semilunar valves. It may be an isolated finding or occur in association with other anomalies. Severe clinical manifestations, such as congestive heart failure or pulmonary hypertension, typically develop in early life.

Disease data
Klasyfikacja

Morphological anomaly

Synonimy
Congenital aortopulmonary artery fistula
Okienko aortalne
Wrodzona przetoka tętnicza aortalno-płucna
Wrodzony ubytek przegrody aortalno-płucnej
Congenital aortopulmonary septal defect
Kod ORPHA
2037
Kod OMIM
-
Kod ICD10
Q21.4
Kod ICD11
LA8B.0

No additional description.

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