Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare congenital non-syndromic heart malformation characterized by a communication between the ascending aorta and the pulmonary trunk in the presence of two normally formed semilunar valves. It may be an isolated finding or occur in association with other anomalies. Severe clinical manifestations, such as congestive heart failure or pulmonary hypertension, typically develop in early life. Disease data Classification Morphological anomaly Synonyms Congenital aortopulmonary artery fistula Okienko aortalne Wrodzona przetoka tętnicza aortalno-płucna Wrodzony ubytek przegrody aortalno-płucnej Congenital aortopulmonary septal defect ORPHA code 2037 OMIM code - ICD10 code Q21.4 ICD11 code LA8B.0 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl