Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Endomyocardial fibroelastosis is a cause of unexplained childhood cardiac insufficiency. It results from diffuse thickening of the endocardium leading to dilated myocardiopathy in the majority of cases and restrictive myocardiopathy in rare cases. It may occur as a primary disorder or may be secondary to another cardiac malformation, notably aortic stenosis or atresia. Disease data Classification Disease Synonyms Endomyocardial fibroelastosis ORPHA code 2022 OMIM code 226000 ICD10 code I42.4 ICD11 code BC43.3 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl