Rasmussen subacute encephalitis

Orpha code: 1929OMIM code:

Definicja

A rare inflammatory and autoimmune disease with epilepsy characterized by unilateral hemispheric atrophy, associated with drug-resistant focal epilepsy, progressive hemiplegia, and cognitive decline. The disease mainly affects children and begins with a prodromal period with mild hemiparesis or infrequent seizures lasting up to several years. The acute stage is marked by frequent seizures arising from one cerebral hemisphere, followed by a residual stage with persistent severe neurological deficits and relapsing epilepsy.

Disease data
Klasyfikacja

Disease

Synonimy
Rasmussen syndrome
Zespół Rasmussena
Kod ORPHA
1929
Kod OMIM
-
Kod ICD10
G04.8
Kod ICD11
8A62.Y

No additional description.

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