OBSOLETE: Primary pigmented nodular adrenocortical disease

Orpha code: 189439OMIM code: 615830

Definition

Primary pigmented nodular adrenocortical disease (PPNAD) is a form of bilateral adrenocortical hyperplasia that is often associated with adrenocorticotrophin hormone (ACTH) independent Cushing syndrome (see this term) and is characterized by small to normal sized adrenal glands containing multiple small cortical pigmented nodules (less than 1 cm in diameter).

Disease data
Classification

Disease

Synonyms
PPNAD
PPNAD
Primary pigmented nodular adrenal dysplasia
ORPHA code
189439
OMIM code
615830
ICD10 code
E24.8
ICD11 code
-

No additional description.

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