Scimitar syndrome

Orpha code: 185OMIM code:

Definition

Scimitar syndrome is characterized by a combination of cardiopulmonary anomalies including partial anomalous pulmonary venous return connection of the right lung to the inferior caval vein leading to the creation of a left-to-right shunt.

Disease data
Classification

Malformation syndrome

Synonyms
Congenital pulmonary venolobar syndrome
Zespół Halasza
Epibronchial right pulmonary vein syndrome
Halasz syndrome
Hypogenetic lung syndrome
ORPHA code
185
OMIM code
-
ICD10 code
Q26.8
ICD11 code
LA86.22

No additional description.

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