Neutrophil immunodeficiency syndrome

Orpha code: 183707OMIM code: 618987

Definicja

Neutrophil immunodeficiency syndrome is a primary immunodeficiency characterized by neutrophilia with severe neutrophil dysfunction, leukocytosis, a predisposition to bacterial infections and poor wound healing, including an absence of pus in infected areas.

Disease data
Klasyfikacja

Disease

Kod ORPHA
183707
Kod OMIM
618987
Kod ICD10
D71
Kod ICD11
4A00.00

No additional description.

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