Odontomicronychial dysplasia

Definition

Odontomicronychial dysplasia is a rare, hereditary ectodermal dysplasia syndrome characterized by involvement of teeth and nails - precocious eruption and shedding of deciduous dentition, precocious eruption of secondary dentition with short, rhomboid roots, and short, thin, slow growing nails.

Disease data

Classification

Malformation syndrome

ORPHA code

1811

OMIM code

601319

ICD10 code

Q84.8

ICD11 code

*Soruce