Didelphys uterus

Orpha code: 180086OMIM code:

Definition

A rare non-syndromic uterovaginal malformation characterized by two separate uterine cavities and cervices, due to failure of the Müllerian ducts to fuse. A longitudinal vaginal septum of variable thickness and elasticity is also present. Patients may be asymptomatic or experience dyspareunia or dysmenorrhea. There is increased frequency of endometriosis, as well as fertility and gestational issues with significantly reduced chances of seeing a pregnancy to term. The condition may be associated with renal agenesis.

Disease data
Classification

Morphological anomaly

Synonyms
Bicervical bicornuate uterus
Macica dwurożna dwuszyjkowa
ORPHA code
180086
OMIM code
-
ICD10 code
Q51.1
ICD11 code
LB44.3

No additional description.

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