Hypomandibular faciocranial dysostosis

Orpha code: 1790OMIM code: 241310

Definicja

Hypomandibular faciocranial dysostosis is a cranial malformation characterized by facial dysmorphism (proptosis, frontal bossing, midface and zygomatic arches hypoplasia, short nose with anteverted nostrils, microstomia with persistent buccopharyngeal membrane, severe hypoglossia with glossoptosis, severe mandibular hypoplasia, and low set ears) associated with laryngeal hypoplasia and craniosynostosis. Other variable features include cleft palate, optic nerve coloboma and choanal stenosis.

Disease data
Klasyfikacja

Malformation syndrome

Kod ORPHA
1790
Kod OMIM
241310
Kod ICD10
Q75.4
Kod ICD11
-

No additional description.

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