Primary cutaneous follicle center lymphoma

Orpha code: 178540OMIM code:

Definition

A rare, indolent primary cutaneous B-cell lymphoma characterized by a solitary or grouped erythematous plaques or tumors, preferentially located on the head, neck or trunk region, and composed of centroblasts and centrocytes arranged in a follicular, diffuse, or mixed growth pattern. The lesions are smooth and typically do not ulcerate. The neoplastic cells express pan B cell markers and Bcl-6, and typically lack Bcl-2.

Disease data
Classification

Disease

Synonyms
PCFCL
PCFCL
ORPHA code
178540
OMIM code
-
ICD10 code
C82.6
ICD11 code
2A80.3

No additional description.

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