Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma is a rare form of primary cutaneous T-cell lymphoma characterized by rapidly progressing, localized or disseminated nodules, tumors or eczematous skin lesions. It has a particularly aggressive clinical course with a high tendency to spread, in advanced stages, to extracutaneous locations (the central nervous system, lung, testes). Lymph nodes are often spared. Disease data Classification Disease Synonyms Berti lymphoma Chłoniak Bertiego Pierwotny skórny chłoniak epidermotropowy cytotoksyczny z komórek T CD8+ Primary cutaneous epidermotropic cytotoxic CD8+ T-cell lymphoma ORPHA code 178528 OMIM code - ICD10 code C84.5 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl