Localized pagetoid reticulosis

Orpha code: 178517OMIM code:

Definition

A rare variant of mycosis fungoides (MF), a form of cutaneous T-cell lymphoma, characterized by the presence of localized patches or plaques with epidermal hyperplasia and intraepidermal proliferation of neoplastic T-cells, usually involving one extremity.

Disease data
Classification

Disease

Synonyms
Pagetoid reticulosis, Woringer-Kolopp type
Siatkowica pagetoidalna, typu Woringera i Koloppa
ORPHA code
178517
OMIM code
-
ICD10 code
C84.0
ICD11 code
-

No additional description.

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