Reticulate acropigmentation of Kitamura

Orpha code: 178307OMIM code: 615537

Definition

A rare, genetic, hyperpigmentation of the skin disease characterized by childhood to adulthood-onset of reticulate, slightly depressed, sharply demarcated, brown, macular skin lesions without hypopigmentation, affecting the dorsa of the hands and feet, and, occasionally, progressing to involve limbs, neck, forehead and/or trunk. Interrupted dermatoglyphics and palmoplantar pits may be additionally observed. Histologically, hyperpigmented lesions show slightly elongated and thinned rete ridges, mild hyperkeratosis without parakeratosis and absence of incontinentia pigmenti.

Disease data
Classification

Disease

Synonyms
RAK
RAPK
ORPHA code
178307
OMIM code
615537
ICD10 code
L81.8
ICD11 code
-

No additional description.

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